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Others—Unicuspid Valve and Quadricuspid Valve

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Aortic Valve Preservation
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Abstract

A unicuspid aortic valve (UAV) is very rare, with a reported occurrence rate of just 0.02% [1]. However, it is also reported that in aortic valve replacement for aortic valve stenosis, a UAV is observed in about 5% of the cases [2], and it cannot be said to be a rare condition for cardiac surgeons. In addition, there are many cases diagnosed as a bicuspid aortic valve (BAV) not only on preoperative examination but also intraoperatively, and the actual frequency is thought to be higher than reported. Furthermore, the quadricuspid aortic valve (QAV) is an even rarer condition, the reported incidence by various researches is less than 0.01% [3]. In this chapter, an understanding of the anatomical knowledge of UAVs and QAVs and valvuloplasty other than mainstream aortic valve replacement and autologous pulmonary valve transplantation by Ross surgery are highlighted with an introduction to past reports and experiences at the facilities where the author used to work in.

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References

  1. Novaro GM, Mishra M, Griffin BP. Incidence and echocardiographic features of congenital unicuspid aortic valve in an adult population. J Heart Valve Dis. 2003;12:674–8.

    PubMed  Google Scholar 

  2. Roberts WC, Ko JM. Frequency by decades of unicuspid, bicuspid, and tricuspid aortic valves in adults having isolated aortic valve replacement for aortic stenosis, with or without associated aortic regurgitation. Circulation. 2005;111:920–5.

    Article  Google Scholar 

  3. Feldman BJ, Khandheria BK, Warnes CA, et al. Incidence, description and functional assessment of isolated quadricuspid aortic valves. Am J Cardiol. 1990;65:937–8.

    Article  CAS  Google Scholar 

  4. Anderson RH. Understanding the structure of the unicuspid and unicommissural aortic valve. J Heart Valve Dis. 2003;12:670–3.

    PubMed  Google Scholar 

  5. Schäfers HJ, Aicher D, Riodionycheva S, Lindinger A, Rädle-Hurst T, Langer F, et al. Bicuspidization of the unicuspid aortic valve: a new reconstructive approach. Ann Thorac Surg. 2008;85:2012–8.

    Article  Google Scholar 

  6. Yamanaka K, Okada K, Okita Y. Aortic root replacement with a valve-sparing technique for quadricuspid aortic valve. Eur J Cardiothorac Surg. 2015;47:741–3.

    Article  Google Scholar 

  7. d’Udekem Y, Siddiqui J, Seaman CS, Konstantinov IE, Galati JC, Cheung MM, et al. Long-term results of a strategy of aortic valve repair in the pediatric population. J Thorac Cardiovasc Surg. 2013;145:461–7.

    Article  Google Scholar 

  8. Tutarel O. The quadricuspid aortic valve: a comprehensive review. J Heart Valve Dis. 2004;13:534–7.

    PubMed  Google Scholar 

  9. Hurwitz LE, Roberts WC. Quadricuspid semilunar valve. Am J Cardiol. 1973;31:623–6.

    Article  CAS  Google Scholar 

  10. Raedle-Hurst TM, Hosse M, Hoffmann S, Abdul-Khaliq H, Schäfers HJ. Ventricular performance assessed by 2-dimensional strain analysis after ross operation versus aortic valve reconstruction. Ann Thorac Surg. 2013;96:1567–73.

    Article  Google Scholar 

  11. Tan Tanny SP, Yong MS, D'Udekem Y, Kowalski R, Wheaton G, D’Orsogna L, et al. Ross procedure in children: 17-year experience at a single institution. J Am Heart Assoc. 2013;2:e000153.

    Article  Google Scholar 

  12. Aicher D, Kunihara T, Abou Issa O, Brittner B, Gräber S, Schäfers HJ. Valve configuration determines long-term results after repair of the bicuspid aortic valve. Circulation. 2011;123:178–85.

    Article  Google Scholar 

  13. Aicher D, Bewarder M, Kindermann M, Abdul-Khalique H, Schäfers HJ. Aortic valve function after bicuspidization of the unicuspid aortic valve. Ann Thorac Surg. 2013;95:1545–50.

    Article  Google Scholar 

  14. Vahanian A, Alfieri O, Andreotti F, et al. Guidelines on the management of valvular heart disease (version 2012): the joint task force on the management of valvular heart disease of the European Society of Cardiology (ESC) and the European Association for Cardio-Thoracic Surgery (EACTS). Eur Heart J. 2012;33:2451–96.

    Article  Google Scholar 

  15. Takahashi H, Aicher D, Kunihara T, Schäfers HJ. Aortic valve repair in patients with unicuspid aortic valve by bicuspidization with augmentation using pericardium. Interact Cardiovasc Thorac Surg. 2013;17:S93.

    Article  Google Scholar 

  16. Franciulli M, Aicher D, Rädle-Hurst T, Takahashi H, Rodionycheva S, Schäfers HJ. Root remodeling and aortic valve repair for unicuspid aortic valve. Ann Thorac Surg. 2014;98:823–9.

    Article  Google Scholar 

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Correspondence to Hiroaki Takahashi .

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Takahashi, H. (2019). Others—Unicuspid Valve and Quadricuspid Valve. In: Kunihara, T., Takanashi, S. (eds) Aortic Valve Preservation. Springer, Singapore. https://doi.org/10.1007/978-981-13-2068-2_13

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  • DOI: https://doi.org/10.1007/978-981-13-2068-2_13

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-13-2067-5

  • Online ISBN: 978-981-13-2068-2

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