Abstract
Pancreaticobiliary maljunction (PBM) is a congenital malformation in which the pancreatic duct and the bile duct join outside of the duodenal wall forming a long common channel. In patients with PBM, biliary tract cancer occurred in 11.1–37.6%, and gallbladder cancer was the most common type of cancer. PBM is frequently accompanied with congenital biliary dilatation (CBD). CBD is a congenital anomaly of the bile duct associated with varying degrees of cystic dilatation at different sites of extrahepatic and intrahepatic bile ducts. In Korea, CBD affects women about three times more frequently. In terms of CBD classification, types I and IVa CBD were the two most common types. Among patients with CBD, 9.9% presented with biliary tract cancer.
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Song, T.J., Kim, MH. (2018). Pancreaticobiliary Maljunction and Congenital Biliary Dilatation in Korea. In: Kamisawa, T., Ando, H. (eds) Pancreaticobiliary Maljunction and Congenital Biliary Dilatation. Springer, Singapore. https://doi.org/10.1007/978-981-10-8654-0_4
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