Peripheral primitive neuroectodermal tumours other than neuroblastoma

Part of the Current Histopathology book series (CUHI, volume 22)


These are extracranial neoplasms arising generally in soft tissues and displaying a primitive microscopic structure in which evidence of neural differentiation is demonstrated. The light microscopic features resemble those of many small-cell tumours, but more especially sympathetic neuroblastoma or Ewing’s sarcomal . Their precise origin is unclear, and they may arise from a pluripotential stem cell. either of embryonic neural crest or mesenchymal origin2. Entities that qualify for inclusion in this category continue to increase in number and complexity1.


Malignant Peripheral Nerve Sheath Tumor Neuroectodermal Tumour Primitive Neuroectodermal Tumour Olfactory Neuroblastoma MIC2 Gene 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© S. Variend 1993

Authors and Affiliations

  1. 1.Department of HistopathologySheffield Children’s HospitalSheffieldUK

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