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Clinical and genetic studies of disorders in fructose metabolism

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Inherited Disorders of Carbohydrate Metabolism

Abstract

Fructose is a major food constituent in human nutrition. In the form of refined sugar its consumption has steadily increased during recent decades. It has been used widely for clinical purposes as it has been claimed to be of advantage for diabetics, and for parenteral nutrition in adults and children. The latter use has remained controversial as many studies have indicated that for infusion therapy glucose is safest and cheapest1,2. The clinical and metabolic aspects of fructose have been discussed at several symposia3–6.

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© 1980 The Society for the Study of Inborn Errors of Metabolism

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Baerlocher, K., Gitzelmann, R., Steinmann, B. (1980). Clinical and genetic studies of disorders in fructose metabolism. In: Burman, D., Holton, J.B., Pennock, C.A. (eds) Inherited Disorders of Carbohydrate Metabolism. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-9215-3_11

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  • DOI: https://doi.org/10.1007/978-94-009-9215-3_11

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