Cystic Diseases of the Kidney
Renal cysts are a heterogeneous group of inherited, developmental and acquired disorders. Despite this non-uniformity, there is value in grouping the types of cystic abnormalities because they share certain characteristics. The major categories of cystic disease are: 1) cystic dysplasia which connotes abnormal renal morphogenesis and differentiation; 2) polycystic disease of both autosomal recessive and autosomal dominant type; 3) medullary cysts of several types including medullary sponge kidney, and the complex of medullary cystic disease; 4) isolated cortical cysts; and 5) inherited syndromes of multiple malformations which are associated with renal cysts.
KeywordsCavitation Proteinuria Triad Pyramid Vasopressin
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