Cystic Diseases of the Kidney

  • Lewis Reisman
  • Matthew R. Kaplan
Part of the Developments in Nephrology book series (DINE, volume 1)


Renal cysts are a heterogeneous group of inherited, developmental and acquired disorders. Despite this non-uniformity, there is value in grouping the types of cystic abnormalities because they share certain characteristics. The major categories of cystic disease are: 1) cystic dysplasia which connotes abnormal renal morphogenesis and differentiation; 2) polycystic disease of both autosomal recessive and autosomal dominant type; 3) medullary cysts of several types including medullary sponge kidney, and the complex of medullary cystic disease; 4) isolated cortical cysts; and 5) inherited syndromes of multiple malformations which are associated with renal cysts.


Renal Cyst Renal Tubular Acidosis Cystic Disease Intravenous Pyelography Salt Wasting 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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© Martinus Nijhoff Publishers bv, The Hague 1981

Authors and Affiliations

  • Lewis Reisman
  • Matthew R. Kaplan

There are no affiliations available

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