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Artificial cell-encapsulated enzymes and adsorbents in congenital metabolic disorders

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Inborn Errors of Metabolism in Humans

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Abstract

The present status of artificial cell-encapsulated enzymes and adsorbents and the feasibility of using them for removing or converting accumulated metabolites will be discussed. For the present discussion it is convenient to divide congenital metabolic disorders1,2 into two major groups: (1) those with extracellular or intracellular accumulation of metabolites, which might be helped by the removal of the metabolites from the extracellular fluid; and (2) those with intracellular accumulation of metabolites which cannot be removed by extracellular means.

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References

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Authors
  1. T. M. S. Chang
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Editors and Affiliations

  1. University Department of Child Health, Royal Hospital for Sick Children, Yorkhill, Glasgow, G3 8SJ, UK

    Forrester Cockburn

  2. Division of Metabolism, University Paediatric Department, Kinderspital, 8032, Zurich, Switzerland

    Richard Gitzelmann

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© 1982 The Society for the Study of Inborn Errors of Metabolism

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Chang, T.M.S. (1982). Artificial cell-encapsulated enzymes and adsorbents in congenital metabolic disorders. In: Cockburn, F., Gitzelmann, R. (eds) Inborn Errors of Metabolism in Humans. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-7325-1_9

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  • DOI: https://doi.org/10.1007/978-94-009-7325-1_9

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-009-7327-5

  • Online ISBN: 978-94-009-7325-1

  • eBook Packages: Springer Book Archive

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