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Abnormal oligodendrocyte differentiation in a mouse mutant with defect in myelination

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Inborn Errors of Metabolism in Humans

Abstract

Animal mutants with myelination defects, particularly those showing a similarity with human diseases, are useful models for the study of inherited neurological disorders.

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References

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Authors
  1. L. Bologa-Sandru
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  2. H.-P. Siegrist
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  3. A. Z’graggen
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  4. U. Wiesmann
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  5. N. Herschkowitz
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Editor information

Editors and Affiliations

  1. University Department of Child Health, Royal Hospital for Sick Children, Yorkhill, Glasgow, G3 8SJ, UK

    Forrester Cockburn

  2. Division of Metabolism, University Paediatric Department, Kinderspital, 8032, Zurich, Switzerland

    Richard Gitzelmann

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© 1982 The Society for the Study of Inborn Errors of Metabolism

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Bologa-Sandru, L., Siegrist, HP., Z’graggen, A., Wiesmann, U., Herschkowitz, N. (1982). Abnormal oligodendrocyte differentiation in a mouse mutant with defect in myelination. In: Cockburn, F., Gitzelmann, R. (eds) Inborn Errors of Metabolism in Humans. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-7325-1_15

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  • DOI: https://doi.org/10.1007/978-94-009-7325-1_15

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-009-7327-5

  • Online ISBN: 978-94-009-7325-1

  • eBook Packages: Springer Book Archive

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