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The Diagnosis and Management of Scleromyxoedema

  • Chapter
Tumours, Lymphomas and Selected Paraproteinaemias

Part of the book series: New Clinical Applications ((NCDM,volume 7))

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Abstract

Scleromyxoedema is a variant of lichen myxoedematosus (papular mucinosis), one of the primary cutaneous mucinoses. The disease is rare and the aetiology is unknown. The characteristic features are (1) infiltrative skin lesions due to deposition of acid mucopolysaccharide in the dermis; (2) normal thyroid function; and (3) a serum paraprotein which is found in most, but not all, cases1. The clinical and histological appearances, paraproteinaemia, complications, and management will be discussed.

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Authors
  1. A. W. Macfarlane
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  2. J. L. Verbov
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Editor information

Editors and Affiliations

  1. Royal Liverpool Hospital, Prescot Street, Liverpool, L7 8XP, UK

    Julian L. Verbov JP, MD, FRCP, FIBiol (Consultant Dermatologist) (Consultant Dermatologist)

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© 1988 Kluwer Academic Publishers

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Macfarlane, A.W., Verbov, J.L. (1988). The Diagnosis and Management of Scleromyxoedema. In: Verbov, J.L. (eds) Tumours, Lymphomas and Selected Paraproteinaemias. New Clinical Applications, vol 7. Springer, Dordrecht. https://doi.org/10.1007/978-94-009-2623-3_5

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  • DOI: https://doi.org/10.1007/978-94-009-2623-3_5

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-010-7683-8

  • Online ISBN: 978-94-009-2623-3

  • eBook Packages: Springer Book Archive

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