Abstract
The epithelioid sarcoma (ES) is a rare, high-grade malignant soft tissue tumor, which shows preference for distal parts of the extremities, particularly the hand. It differ from benign lesions (e.g. ganglion) in ways of that are often non apparent until there is recurrence. Regional lymph node involvement and distant metastases (lungs) are often apparent. Treatment of the ES includes the primary radical surgical excision, sometimes combined with sentinel lymph node biopsy and radiation or chemotherapy. Amputation of the affected fingers is necessary in all cases of recurrence but might be avoided in initial surgery with respect to pediatric patients and maximal function. Consequently, soft tissue defects must be treated following plastic surgical principles. Close oncological follow-ups are inevitable, since there can be tumor recurrence even years after resection of the primary tumor.
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Stang, F., Mailänder, P., Siemers, F. (2013). Pediatric Epitheloid Finger Sarcoma: Diagnosis and Treatment. In: Hayat, M. (eds) Pediatric Cancer, Volume 4. Pediatric Cancer, vol 4. Springer, Dordrecht. https://doi.org/10.1007/978-94-007-6591-7_23
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DOI: https://doi.org/10.1007/978-94-007-6591-7_23
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