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Chordomas of the Clivus and Upper Cervical Spine

  • David ChoiEmail author
Chapter
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Part of the Tumors of the Central Nervous System book series (TCNS, volume 6)

Abstract

Chordomas are challenging tumours which usually occur in the axial ­skeleton, and are particularly difficult to manage when they are situated in the clivus and upper cervical spine due to the proximity of eloquent structures. They also have a tendency for local recurrence since enbloc resection is rarely possible in these locations. They have characteristic radiological appearances on MRI, and pathologically are characterised by the presence of Physallipherous cells. The mainstay of treatment is maximal tumour excision at the time of first presentation, followed by high dose radiation treatment such as proton beam irradiation.

Keywords

Chordoma Cervical spine Clivus Tumor Surgery 

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Copyright information

© Springer Science+Business Media B.V. 2012

Authors and Affiliations

  1. 1.National Hospital for Neurology and NeurosurgeryLondonUK

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