Chordomas of the Clivus and Upper Cervical Spine
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Chordomas are challenging tumours which usually occur in the axial skeleton, and are particularly difficult to manage when they are situated in the clivus and upper cervical spine due to the proximity of eloquent structures. They also have a tendency for local recurrence since enbloc resection is rarely possible in these locations. They have characteristic radiological appearances on MRI, and pathologically are characterised by the presence of Physallipherous cells. The mainstay of treatment is maximal tumour excision at the time of first presentation, followed by high dose radiation treatment such as proton beam irradiation.
KeywordsChordoma Cervical spine Clivus Tumor Surgery
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