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Congenitaal gecorrigeerde transpositie van de grote arteriën

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Bij een congenitaal gecorrigeerde transpositie van de grote arteriën (ccTGA ) is er een normale positie van de atria (situs solitus), maar zijn de atria aangesloten op de ‘verkeerde’ ventrikel (RA op LV en LA op RV), terwijl tevens de aorta uit de RV ontspringt en de art. pulmonalis uit de LV. Er zijn dus discordante AV-connecties en discordante VA-connecties . De circulatie is al tijdens de aanleg van het hart ‘gecorrigeerd’, omdat het bloed op zich goed circuleert: zuurstofarm bloed gaat naar de longen en zuurstofrijk bloed naar het lichaam. ‘Gecorrigeerd’ betekent in dit kader dus niet een operatie! Er is sprake van inversie van de ventrikels waardoor de anatomische RV moet functioneren als systeemventrikel. De LV is de subpulmonale ventrikel . De AV-kleppen volgen de ventrikels, dus de tricuspidalisklep is de systemische AV-klep (figuur 16.1).

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Roos-Hesselink, J., van Dijk, A. (2013). Congenitaal gecorrigeerde transpositie van de grote arteriën. In: Mulder, B., Pieper, P., Meijboom, F., Hamer, J. (eds) Aangeboren hartafwijkingen bij volwassenen. Bohn Stafleu van Loghum, Houten. https://doi.org/10.1007/978-90-368-0307-6_16

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  • DOI: https://doi.org/10.1007/978-90-368-0307-6_16

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