Abstract
Dystonia is a movement disorder in which sustained involuntary muscle contractions result in twisting and repetitive movements or abnormal postures.
Dystonia may be: (a) inherited, (b) acquired, and (c) idiopathic. A specific molecular genetic mutation has been identified for 12 forms; DYT1 is the mutated gene of the early-onset primary dystonia (before age 24 years).
Primary forms are usually slowly progressive. In most individuals with onset in one leg, dystonia progresses over several years. Prognosis of secondary dystonia depends on the underlying disease.
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Quatrale, R. (2015). Extrapyramidal Diseases: Dystonia. In: Sghirlanzoni, A., Lauria, G., Chiapparini, L. (eds) Prognosis of Neurological Diseases. Springer, Milano. https://doi.org/10.1007/978-88-470-5755-5_33
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DOI: https://doi.org/10.1007/978-88-470-5755-5_33
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