Abstract
Pseudomyxoma peritonei (PMP) is a rare, low-grade, peritoneal malignancy predominated by mucus, with an estimated incidence of two to three cases per million people per year [1]. Werth, in 1884, first described PMP as a rare, unusual reaction of the peritoneum to a jelly-like substance, looking like a myxoma, in relation to an ovarian neoplasm [2]. In 1901, Frankel described PMP associated with an appendiceal cyst [3], but the first description of a benign mucocele of the appendix was reported by Rokitansky in 1842 [4].
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Vaira, M., Robella, M., Mellano, A., De Simone, M. (2015). Pseudomyxoma Peritonei. In: Di Giorgio, A., Pinto, E. (eds) Treatment of Peritoneal Surface Malignancies. Updates in Surgery. Springer, Milano. https://doi.org/10.1007/978-88-470-5711-1_16
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DOI: https://doi.org/10.1007/978-88-470-5711-1_16
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