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Esophageal Achalasia

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Pediatric Thoracic Surgery

Abstract

Esophageal achalasia (EA) is a functional disorder characterized by abnormal motility of the esophageal body associated with delayed (or absent) mechanical (but not neurogenic) relaxation of the lower esophageal sphincter (LES) during deglutition. Subsequent dilation of the overhanging esophagus, together with the primary hypoperistalsis, results in ineffective propulsion. EA in the pediatric population is rare, but several cases in late childhood have been described [1–8].

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Author information

Authors and Affiliations

  1. Department of Pediatric Surgery, G. Gaslini Children’s Hospital, Genoa, Italy

    Marcello Carlucci

Authors
  1. Marcello Carlucci
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  2. Girolamo Mattioli
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  3. Vincenzo Jasonni
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Corresponding author

Correspondence to Marcello Carlucci .

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Editors and Affiliations

  1. Pediatric Surgery, University of Bologna, Bologna, Italy

    Mario Lima

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Carlucci, M., Mattioli, G., Jasonni, V. (2013). Esophageal Achalasia. In: Lima, M. (eds) Pediatric Thoracic Surgery. Springer, Milano. https://doi.org/10.1007/978-88-470-5202-4_14

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  • DOI: https://doi.org/10.1007/978-88-470-5202-4_14

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-5201-7

  • Online ISBN: 978-88-470-5202-4

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