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How to Diagnose and Manage Right Ventricular Cardiomyopathy Today

  • T. Wichter
  • M. Borggrefe
  • G. Breithardt

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a frequent cause of ventricular tachyarrhythmias and cardiac arrest in young patients with apparently normal hearts. The cardiomyopathy is characterized by a localized or generalized myocardial atrophy predominantly affecting the right ventricle with subsequent infiltration by fatty and fibrous tissue [1]. The arrhythmogenic substrate is formed by islands of surviving strands of hypertrophied myocytes, predisposing for localized slow conduction and reentrant arrhythmias. The predominant sites of involvement in ARVC are the outflow tract, apex and subtricuspid area of the right ventricle, which were described as the “triangle of dysplasia” [2]. Left ventricular involvement has been described in patients with extensive ARVC and a long history of arrhythmias [3].

Keywords

Ventricular Tachycardia Catheter Ablation Endomyocardial Biopsy Arrhythmogenic Right Ventricular Cardiomyopathy Ventricular Tachyarrhythmia 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Italia 1998

Authors and Affiliations

  • T. Wichter
    • 1
  • M. Borggrefe
    • 1
  • G. Breithardt
    • 1
  1. 1.Department of Cardiology and AngiologyHospital of the Westfälische Wilhelms-University and Institute for Arteriosclerosis ResearchMünsterGermany

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