Focus on Pathophysiology, Diagnosis and Management of Chronic Thromboembolic Disease

  • I. Lang
  • M. Kneussl
Conference paper


CTEPH is the result of single or recurrent pulmonary thromboemboli arising from sites of venous thrombosis. The natural history of pulmonary thromboemboli is to undergo total resolution, or resolution leaving minimal residua, with restoration of normal pulmonary haemodynamics. For reasons still unclear, thromboemboli in CTEPH patients fail to resolve and form endothelialised obstructions of the pulmonary vascular bed including the major branches.


Pulmonary Vascular Resistance Primary Pulmonary Hypertension Pulmonary Angiography Chronic Thromboembolic Pulmonary Hypertension CTEPH Patient 
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Copyright information

© Springer-Verlag Italia 2000

Authors and Affiliations

  • I. Lang
  • M. Kneussl

There are no affiliations available

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