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Hypertrophic Cardiomyopathy and Sudden Death in the Young: a Pathologist’s View

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Abstract

Hypertrophic cardiomyopathy (HCM) is a highly arrhythmogenic primary heart muscle disease. Clinical manifestations are variable ranging from a benign asymptomatic course to severe heart failure and cardiac arrest. Ventricular arrhythmias, palpitations and syncope are frequent signs and symptoms. Sudden, unexpected cardiac arrest is a pending catastrophe in the natural history of HCM.

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© 1998 Springer-Verlag Italia

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Basso, C., Corrado, D., Angelini, A., Thiene, G. (1998). Hypertrophic Cardiomyopathy and Sudden Death in the Young: a Pathologist’s View. In: Camerini, F., Gavazzi, A., De Maria, R. (eds) Advances in Cardiomyopathies. Springer, Milano. https://doi.org/10.1007/978-88-470-2155-6_8

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  • DOI: https://doi.org/10.1007/978-88-470-2155-6_8

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-2181-5

  • Online ISBN: 978-88-470-2155-6

  • eBook Packages: Springer Book Archive

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