Effect of β-Blocker Therapy on the Frequency and Type of Cardiac Events in Patients with the Hereditary Long QT Syndrome
The hereditary long QT syndrome (LQTS) is a genetic channelopathy in which affected individuals have prolonged ventricular repolarization, frequent syncopal episodes, and a propensity to sudden arrhythmic cardiac death [1, 2]. β-Blocker therapy is the recommended treatment of choice for this disorder, although other forms of therapy are also used including pacemakers to prevent bradycardia- induced ventricular tachyarrhythmias , surgical antiadrenergic therapy with left cervico-thoracic sympathetic ganglionectomy , and implantable car- dioverter defibrillators  in patients refractory to β-blocker therapy.
KeywordsCardiac Event Affect Family Member Blocker Therapy Blocker Treatment Implantable Cardioverter Defibrillator Therapy
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