Abstract
The hereditary long QT syndrome (LQTS) is a genetic channelopathy in which affected individuals have prolonged ventricular repolarization, frequent syncopal episodes, and a propensity to sudden arrhythmic cardiac death [1, 2]. β-Blocker therapy is the recommended treatment of choice for this disorder, although other forms of therapy are also used including pacemakers to prevent bradycardia- induced ventricular tachyarrhythmias [3], surgical antiadrenergic therapy with left cervico-thoracic sympathetic ganglionectomy [4], and implantable car- dioverter defibrillators [5] in patients refractory to β-blocker therapy.
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References
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© 2000 Springer-Verlag Italia
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Moss, A.J., Zareba, W., Hall, W.J., Robinson, J.L., Andrews, M.L. (2000). Effect of β-Blocker Therapy on the Frequency and Type of Cardiac Events in Patients with the Hereditary Long QT Syndrome. In: Raviele, A. (eds) Cardiac Arrhythmias 1999. Springer, Milano. https://doi.org/10.1007/978-88-470-2139-6_39
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DOI: https://doi.org/10.1007/978-88-470-2139-6_39
Publisher Name: Springer, Milano
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