Slit Ventricle Syndrome or Syndromes: Diagnosis and Management

  • Harold L. Rekate


The term “slit ventricle syndrome” (SVS) is widely used to describe a condition of severe, usually intermittent, headaches suffered by patients with longstanding ventricular shunting for hydrocephalus [15,16,20]. It is important to differentiate this condition from the smaller than normal, even almost nonexistent ventricles seen in some patients on routine imaging studies. The finding of radiographic slit ventricles occurs in at least 85% of children who are shunted and has been said to be a “goal” of shunting (M.L. Walker, personal communication, 1986). Most of these patients are asymptomatic and require no intervention. Only when patients begin to suffer from a severe headache disorder that interferes with their normal lives does the presence of radiographic slit ventricles lead to the diagnosis of the SVS.


Spina Bifida Endoscopic Third Ventriculostomy Intracranial Hypotension Ventricular Catheter Shunt Failure 
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Copyright information

© Springer-Verlag Italia 2005

Authors and Affiliations

  • Harold L. Rekate
    • 1
  1. 1.Pediatric Neurosciences, Division of Neurological Surgery, Barrow Neurological InstituteSt. Joseph’s Hospital and Medical CenterPhoenixUSA

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