Neonatology pp 675-681 | Cite as

Esophageal Atresia

  • Alfredo Garzi
  • Mario Messina


Esophageal atresia includes a group of congenital anomalies characterized as interruption of the continuity of the esophagus combined with or without a persistent communication with the trachea [1]. These congenital malformations occur in 1:2500–3000 live births. The overwhelming majority of cases of esophageal atresia are sporadic/non-syndromic, although a small number within this non-familial group are associated with chromosomal abnormalities [1]. Familial/syndromic cases of esophageal atresia are extremely rare, representing less than 1% of the total. Esophageal atresia is 2–3 times more common in twins [2].


Distal Esophagus Esophageal Atresia Azygos Vein Renal Agenesis Tracheoesophageal Fistula 
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Copyright information

© Springer-Verlag Italia 2012

Authors and Affiliations

  • Alfredo Garzi
    • 1
  • Mario Messina
  1. 1.Department of Pediatrics, Obstetrics and Reproductive Medicine, Section of Pediatric SurgeryPoliclinico Le ScotteSienaItaly

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