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Surgical Treatment of Biliary Tract Malformations

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Abstract

Biliary atresia (BA) is a progressive necroinflammatory process involving the extrahepatic biliary tree, either partially or completely. The disease shows the onset during the first days of life and usually evolves into obliteration of the extrahepatic bile duct lumen with interruption of bile flow, resulting in cholestasis and chronic liver damage. If untreated, the disease leads to exitus within the first 2 years of life. Early diagnosis is mandatory to plan a timely surgery, preferably within 80 days of life.

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Author information

Authors and Affiliations

  1. Pediatric Surgery Unit, University of Brescia, Spedali Civili, Brescia, Italy

    Pierluigi Pedersini

Authors
  1. George Ekema
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  2. Pierluigi Pedersini
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Editor information

Editors and Affiliations

  1. Department of Pediatrics, Obstetrics and Reproductive Medicine, Division of Neonatology, University of Siena General Hospital S. Maria alle Scotte Azienda Ospedaliera Universitaria Senese, Siena, Italy

    Giuseppe Buonocore (Professor of Pediatrics and Neonatology, Head of School of Pediatrics) (Professor of Pediatrics and Neonatology, Head of School of Pediatrics)

  2. University of Siena, Siena, Italy

    Rodolfo Bracci (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine) (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine)

  3. University of Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  4. Department of Women’s and Children’s Health, Institute of Translational Medicine, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  5. Liverpool Women’s Hospital, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

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© 2012 Springer-Verlag Italia

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Ekema, G., Pedersini, P. (2012). Surgical Treatment of Biliary Tract Malformations. In: Buonocore, G., Bracci, R., Weindling, M. (eds) Neonatology. Springer, Milano. https://doi.org/10.1007/978-88-470-1405-3_87

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  • DOI: https://doi.org/10.1007/978-88-470-1405-3_87

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-1404-6

  • Online ISBN: 978-88-470-1405-3

  • eBook Packages: MedicineMedicine (R0)

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