Neonatology pp 819-821 | Cite as

Neonatal Hereditary Neutropenia

  • Gaetano Chirico
  • Carmelita D’Ippolito


Hereditary neutropenia includes many disorders of distinct origin and variable prognosis, characterized by a reduction of the absolute neutrophil count (ANC) that predisposes patients to bacterial infections, in particular pyogenic infections, such as cutaneous cellulitis, deep abscesses, pneumonia and sepsis [1, 2]. Susceptibility to bacterial infections, even in patients with severe neutropenia, can be quite variable, depending on the underlying etiology. Congenital neutropenia my be associated with extraematopoietic manifestations.


Acute Myeloid Leukemia Neutrophil Elastase Glycogen Storage Disease Autosomal Recessive Disease Exocrine Pancreatic Insufficiency 
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Copyright information

© Springer-Verlag Italia 2012

Authors and Affiliations

  • Gaetano Chirico
    • 1
  • Carmelita D’Ippolito
  1. 1.Neonatology and Neonatal Intensive Care UnitSpedali Civili HospitalBresciaItaly

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