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Neonatal Hereditary Neutropenia

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Neonatology

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Abstract

Hereditary neutropenia includes many disorders of distinct origin and variable prognosis, characterized by a reduction of the absolute neutrophil count (ANC) that predisposes patients to bacterial infections, in particular pyogenic infections, such as cutaneous cellulitis, deep abscesses, pneumonia and sepsis [1, 2]. Susceptibility to bacterial infections, even in patients with severe neutropenia, can be quite variable, depending on the underlying etiology. Congenital neutropenia my be associated with extraematopoietic manifestations.

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Author information

Authors and Affiliations

  1. Neonatology and Neonatal Intensive Care Unit, Spedali Civili Hospital, Brescia, Italy

    Gaetano Chirico

Authors
  1. Gaetano Chirico
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  2. Carmelita D’Ippolito
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Editor information

Editors and Affiliations

  1. Department of Pediatrics, Obstetrics and Reproductive Medicine, Division of Neonatology, University of Siena General Hospital S. Maria alle Scotte Azienda Ospedaliera Universitaria Senese, Siena, Italy

    Giuseppe Buonocore (Professor of Pediatrics and Neonatology, Head of School of Pediatrics) (Professor of Pediatrics and Neonatology, Head of School of Pediatrics)

  2. University of Siena, Siena, Italy

    Rodolfo Bracci (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine) (Formerly Professor of Pediatrics and Head of Department of Pediatrics, Obstetrics and Reproductive Medicine)

  3. University of Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  4. Department of Women’s and Children’s Health, Institute of Translational Medicine, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

  5. Liverpool Women’s Hospital, Liverpool, UK

    Michael Weindling (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery) (Professor of Perinatal Medicine, Director of Postgraduate Research, Head of School of Paediatrics Mersey Deanery)

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© 2012 Springer-Verlag Italia

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Chirico, G., D’Ippolito, C. (2012). Neonatal Hereditary Neutropenia. In: Buonocore, G., Bracci, R., Weindling, M. (eds) Neonatology. Springer, Milano. https://doi.org/10.1007/978-88-470-1405-3_106

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  • DOI: https://doi.org/10.1007/978-88-470-1405-3_106

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-1404-6

  • Online ISBN: 978-88-470-1405-3

  • eBook Packages: MedicineMedicine (R0)

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