Vascular Malformations of the Pediatric Chest

  • M. J. Siegel


The left aortic arch with an aberrant right subclavian artery is the most common congenital abnormality of the aortic arch vessels and occurs in about 0.5–2% of the population [1, 2] (Fig. 1). The right subclavian artery is the last of the major arteries to arise from the aortic arch; thus, the order of branching is right common carotid, left common carotid, left subclavian, and right subclavian. A diverticulum-like outpouching, referred to as a Kommerell diverticulum, may be seen at the site of origin of the aberrant vessel. Patients are usually asymptomatic, since this lesion does not represent a true vascular-ring anomaly.


Aortic Arch Pulmonary Vein Subclavian Artery Patent Ductus Arteriosus Left Pulmonary Artery 
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© Springer-Verlag Italia 2007

Authors and Affiliations

  • M. J. Siegel
    • 1
  1. 1.Mallinckrodt Institute of RadiologyWashington University School of MedicineSt. LouisUSA

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