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Pulmonary Manifestations of Systemic Diseases

  • C. Schaefer-Prokop

Abstract

The following review focuses on pulmonary manifestations of granulomatous diseases (sarcoidosis), connective tissue diseases, vasculitis (Wegener granulomatosis and Church-Strauss), and Goodpasture syndrome. Rare pulmonary manifestations associated with other diseases, such as tuberous sclerosis and lymphangioleiomyomatosis, Erdheim-Chester disease (rare non-Langerhans cell histiocytosis), storage diseases (Gaucher, Niemann Pick), systemic amyloidosis, and relapsing polychondritis, as well as manifestations of neoplastic diseases (e.g., lymphoma) are not considered herein. Langerhans cell histiocytosis shows a pulmonary involvement that is associated with a systemic manifestation only in children and not in adults.

Keywords

Idiopathic Pulmonary Fibrosis High Resolution Compute Tomography Usual Interstitial Pneumonia Progressive Systemic Sclerosis Cryptogenic Organize Pneumonia 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Italia 2007

Authors and Affiliations

  • C. Schaefer-Prokop
    • 1
  1. 1.Department of RadiologyAcademic Medical CenterAmsterdamThe Netherlands

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