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Pulmonary Manifestations of Systemic Diseases

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Diseases of the Heart, Chest & Breast

Abstract

The following review focuses on pulmonary manifestations of granulomatous diseases (sarcoidosis), connective tissue diseases, vasculitis (Wegener granulomatosis and Church-Strauss), and Goodpasture syndrome. Rare pulmonary manifestations associated with other diseases, such as tuberous sclerosis and lymphangioleiomyomatosis, Erdheim-Chester disease (rare non-Langerhans cell histiocytosis), storage diseases (Gaucher, Niemann Pick), systemic amyloidosis, and relapsing polychondritis, as well as manifestations of neoplastic diseases (e.g., lymphoma) are not considered herein. Langerhans cell histiocytosis shows a pulmonary involvement that is associated with a systemic manifestation only in children and not in adults.

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Authors and Affiliations

  1. Department of Radiology, Academic Medical Center, Amsterdam, The Netherlands

    C. Schaefer-Prokop

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  1. C. Schaefer-Prokop
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Editors and Affiliations

  1. Department of Radiology, University Hospital Balgrist, Zurich, Switzerland

    J. Hodler

  2. Kantonsspital, Institut für Radiologie, Winterthur, Switzerland

    Ch. L. Zollikofer

  3. Nuklearmedizin, Universitätsspital, Zurich, Switzerland

    G. K. von Schulthess

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© 2007 Springer-Verlag Italia

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Schaefer-Prokop, C. (2007). Pulmonary Manifestations of Systemic Diseases. In: Hodler, J., Zollikofer, C.L., von Schulthess, G.K. (eds) Diseases of the Heart, Chest & Breast. Springer, Milano. https://doi.org/10.1007/978-88-470-0633-1_19

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  • DOI: https://doi.org/10.1007/978-88-470-0633-1_19

  • Publisher Name: Springer, Milano

  • Print ISBN: 978-88-470-0632-4

  • Online ISBN: 978-88-470-0633-1

  • eBook Packages: MedicineMedicine (R0)

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