Management of Heart Failure

  • Elzbieta Katarzyna Wlodarska
  • Marek Konka


Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) has long been considered a disease with the risk of sudden cardiac death (SCD) [1, 2]. Life-threatening arrhythmias have been emphasized as the main clinical feature and major therapeutic problem. In long-term follow-up studies, high rates of SCD have been reported, particularly in the young. Enormous progress has been made in recent years in the treatment of arrhythmias, changing the clinical outcome of ARVC/D. Implantable cardioverter- defibrillator (ICD) implantation, radiofrequency (RF) ablation or hybrid therapy for high-risk patients have significantly decreased the incidence of SCD in this group of patients.Worldwide awareness of the disease, advances in diagnostic procedures, preparticipation screening tests of young athletes, and family examinations have identified affected people early and enabled proper management, decreasing the incidence of SCD as the first symptom of the disease. Success in the fight against SCD unmasked the problem of heart failure in patients with a longer disease history.


Sudden Cardiac Death Right Ventricle Heart Failure Symptom Ventricular Cardiomyopathy Arrhythmogenic Right Ventricular Dysplasia 
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Copyright information

© Springer-Verlag Italia 2007

Authors and Affiliations

  • Elzbieta Katarzyna Wlodarska
    • 1
  • Marek Konka
    • 1
  1. 1.Department of Congenital Heart DiseaseInstitute of CardiologyWarsawPoland

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