The Role of the Implantable Cardiac Defibrillator in the Management

  • Olaf Hedrich
  • Gianfranco Buja
  • Domenico Corrado
  • Mark S. Link
  • Thomas Wichter
  • N. A. Mark EstesIII


The management of patients with arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) has evolved considerably over the last several years. Because many patients with ARVC/D may be at risk for sudden cardiac death (SCD) and clinical series have reported favorable outcomes with this therapy, the implantable cardioverter-defibrillator (ICD) has assumed a larger role in therapy. On the basis of collective observations from several series of patients, implantation of an ICD in a patient with ARVC/D has a major impact on decreasing the risk of SCD. This chapter examines the available clinical information regarding ICD therapy in patients with ARVC/D.


Sudden Death Sudden Cardiac Death Ventricular Cardiomyopathy Implantable Cardiac Defibrillator Arrhythmogenic Right Ventricular Dysplasia 
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Copyright information

© Springer-Verlag Italia 2007

Authors and Affiliations

  • Olaf Hedrich
    • 1
  • Gianfranco Buja
    • 2
  • Domenico Corrado
    • 2
  • Mark S. Link
    • 1
  • Thomas Wichter
    • 3
  • N. A. Mark EstesIII
    • 4
  1. 1.Cardiac Arrhythmia ServiceTufts-New England Medical CenterBostonUSA
  2. 2.Department of Cardiological, Thoracic and Vascular SciencesUniversity of PaduaItaly
  3. 3.Department of Cardiology and AngiologyUniversity Hospital of MünsterMünsterGermany
  4. 4.New England Cardiac Arrhythmia Center, Tufts-New England Medical CenterTufts University School of MedicineBostonUSA

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