Diagnostic Role of Angiography

  • Thomas Wichter
  • Julia Indik
  • Luciano Daliento


Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by regional or global abnormalities of right ventricular (RV) structure and function and ventricular tachyarrhythmias including sudden death [1, 2]. It is an inheritable cardiomyopathy predominantly affecting the myocardium of the RV free wall. Progressive atrophy and loss of myocytes with subsequent fatty and/or fibrous tissue replacement and interspersed surviving myocyte fibers provide the morphological substrate for re-entrant arrhythmias and regional (segmental) or global (diffuse) abnormalities of RV structure and function. In the advanced stages of ARVC/D, clinical signs of right or global heart failure and left ventricular (LV) involvement may develop [3].


Right Ventricular Right Ventricular Outflow Tract Right Ventricular Dysfunction Right Ventricular Ejection Fraction Tricuspid Annulus Plane Systolic Excursion 
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Copyright information

© Springer-Verlag Italia 2007

Authors and Affiliations

  • Thomas Wichter
    • 1
  • Julia Indik
    • 2
  • Luciano Daliento
    • 1
  1. 1.Department of Cardiology and AngiologyUniversity Hospital of MünsterMünsterGermany
  2. 2.Department of Cardiology, Sarver Heart CenterUniversity of Arizona College of MedicineTucsonUSA

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