Cardiac imaging plays a key role in the evaluation of a patient suspected of having arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D). Global or regional abnormalities of right ventricular (RV) structure and function are an important component of the Task Force of the Working Group on Cardiomyopathies diagnostic criteria . The criterion for RV structure and function currently lacks quantitative cut points for clinicians to use when facing the study of an individual suspected of ARVC/D. Moreover, the ability to correctly categorize individuals at risk for ARVC/D, such as family members of affected individuals or those who may have a subclinical form of the disease, is limited by the lack of a gold standard for the diagnosis of ARVC/D. Additionally, the echocardiographic natural history of the disease has not yet been defined.
KeywordsRight Ventricu Right Ventricular Outflow Tract Right Ventricu Function Right Ventricu Dysfunction Myocardial Performance Index
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