Intraocular Lymphoma


Intraocular lymphoma is a relatively rare and highly malignant disease. The so-called primary intraocular lymphoma (PIOL) may occur prior or subsequent to primary central nervous system (CNS) lymphoma. Intraocular lymphoma is easily misdiagnosed as uveitis, and the issue of masquerade syndrome tends to delay diagnosis and treatment. The prognosis of visual function is similar to other fundus diseases; visual function is often well preserved if the lesion does not involve the macula or optic nerve. However, CNS lymphoma occurs in 65–90 % of the patients [1, 2], and the prognosis of survival is very poor with 5-year survival rate of 30–60 % [3, 4].


Retinal Pigment Epithelium Primary Central Nervous System Lymphoma Cystoid Macular Edema Central Nervous System Lymphoma Central Nervous System Lesion 


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Copyright information

© Springer India 2016

Authors and Affiliations

  1. 1.Department of OphthalmologyTokyo Medical UniversityTokyoJapan

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