Klippel-Trenaunay Syndrome

  • Riju Ramachandran Menon


Klippel-Trenaunay syndrome is a rare sporadic complex congenital abnormality characterized clinically by the triad of capillary malformations (port-wine stain), soft tissue and bone hypertrophy or hypotrophy of one lower limb, and lateral varicosity with or without deep vein anomalies. It is a mixed vascular malformation with predominant capillary, venous, and lymphatic components [1]. It is often mistakenly identified as AV malformation. This chapter deals with the following aspects of this disease:


Vascular Malformation Varicose Vein Venous Malformation Superficial Vein Capillary Hemangioma 
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Copyright information

© Springer India 2015

Authors and Affiliations

  1. 1.General SurgeryAmrita Institute of Medical Sciences, Amrita LaneKochiIndia

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