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Clinical Features of Moyamoya Disease: An Overview

  • Yong-Seung Hwang

Abstract

The two cardinal clinical features of moyamoya disease are ischemic attacks or intracranial hemorrhages. However, the main clinical presentations of moyamoya disease differ substantially between children and adults. Most children with moyamoya disease develop transient ischemic attacks (TIA) or cerebral infarction, whereas about half of the adult patients develop intracranial hemorrhage, and half develop TIA or cerebral infarction, or both [1]. Regarding the ethnic difference, clinical features and the course of moyamoya disease in whites clearly differ from moyamoya disease in Asians in the timing of the onset of vasculopathy and lower rate of hemorrhage [2].

Keywords

Cerebral Infarction Transient Ischemic Attack Basilar Artery Intracranial Aneurysm Moyamoya Disease 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer 2010

Authors and Affiliations

  1. 1.Department of PediatricsPediatric Clinical Neuroscience Center, Seoul National University Children's Hospital, Seoul National University College of MedicineJongno-guRepublic of Korea

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