Is angiomyolipoma a neoplasm or a hamartoma? Does cytologic atypia seen in angiomyolipomas denote aggressive behavior? Does an angiomyolipoma need treatment if it is benign? What is the indication for surgical intervention if it is required?


Renal angiomyolipoma is a benign neoplasm, not a hamartoma. Angiomyolipoma may be included in a group of tumors of perivascular epithelioid cells (PEComas). Renal angiomyolipoma occurs as either a sporadic form or a hereditary form as a part of syndrome of tuberous sclerosis.


Tuberous Sclerosis Cytologic Atypia Renal Angiomyolipoma Perivascular Epithelioid Cell Subependymal Giant Cell Astrocytoma 
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