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The Probability of Developing Familial Adenomatous Polyposis: Combining the Diminishing Risks with Age with Negative Screening at Advancing Age and Linked Gene Markers

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Abstract

Familial Adenomatous Polyposis (FAP) is a rare dominantly inherited disorder characterized by multiple premalignant polyposis in the colon and rectum, occasional polyps in the upper gastro-intestinal tract and other extra-intestinal manifestations including osteomas and epidermoid cysts, desmoid formation, congenital hypertrophy of retinal pigment and other malignant changes including in the thyroid gland.

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References

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© 1990 Springer Japan

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Slack, J. (1990). The Probability of Developing Familial Adenomatous Polyposis: Combining the Diminishing Risks with Age with Negative Screening at Advancing Age and Linked Gene Markers. In: Utsunomiya, J., Lynch, H.T. (eds) Hereditary Colorectal Cancer. Springer, Tokyo. https://doi.org/10.1007/978-4-431-68337-7_11

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  • DOI: https://doi.org/10.1007/978-4-431-68337-7_11

  • Publisher Name: Springer, Tokyo

  • Print ISBN: 978-4-431-68339-1

  • Online ISBN: 978-4-431-68337-7

  • eBook Packages: Springer Book Archive

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