Moyamoya Disease in Hong Kong

  • H. L. Wen
  • Z. D. Mehal
  • John C. K. Kwok
  • Y. W. Chan
  • C. S. Kay


Moyamoya disease is a rare chronic occlusive cerebrovascular disease which was first described as a type of occlusive disease of the internal carotid artery [15, 24]. The clinical pictures of the disease are variable, presenting as hemiplegia, paraplegia, convulsive seizures, headaches, speech disturbances, involuntary movements of the extremities, and mental retardation. The peak age incidence cycle appeared between one to five years and another at 30 years of age. However, the clinical pictures are different between these two groups. The patients under 15 years old often showed recurrent episodes of ischemic cerebrovascular accidents which produced permanent speech or mental defect. In the adult the mode of presentation is signs and symptoms of subarachnoid hemorrhage with poor prognosis.


Internal Carotid Artery Subarachnoid Hemorrhage Moyamoya Disease Cerebral Angiography Intracerebral Hematoma 
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Copyright information

© Springer Japan 1988

Authors and Affiliations

  • H. L. Wen
    • 1
  • Z. D. Mehal
    • 1
  • John C. K. Kwok
    • 1
  • Y. W. Chan
    • 2
  • C. S. Kay
    • 2
  1. 1.Departments of NeurosurgeryKwong Wah HospitalKowloonHong Kong
  2. 2.Departments of NeurologyKwong Wah HospitalKowloonHong Kong

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