Moyamoya Disease in Taiwan

  • Chun-Jen Shih
  • Chain-Fa Su


“Moyamoya”, a word indicating a puff of smoke, names a disease showing stenosis or occlusion of the intracranial arteries at the base of skull and abnormal vascular networks (intraparenchymatous anastomosis) in the region of the basal ganglia. It was first described, on angiography, by Nomura [5] and Takeuchi [8]. A variety of synonyms have been suggested, including “cerebral juxtabasilar telengiectasis,” “cerebral arterial rete,” “rete mirabile,” and “cerebral arterial rete mirabile.” Previously considered to be confined to Japan, moyamoya disease has recently been reported sporadically all over the world [2–4, 6]. In Taiwan, this rare disease is occasionally uncovered at large neurological centers. However, the epidermiology of the disease is, as yet, unclear. In the present joint study, 26 cases were retrospectively assesed in order to delineate the general aspects of this disease in Taiwan.


Moyamoya Disease Cerebral Angiography Cerebral Vascular Accident Intracranial Internal Carotid Artery Juvenile Case 
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Copyright information

© Springer Japan 1988

Authors and Affiliations

  • Chun-Jen Shih
    • 1
  • Chain-Fa Su
    • 2
  1. 1.Department of HealthThe Executive YuanRepublic of China
  2. 2.Department of SurgeryNational Defense Medical Center and Tri-Service General HospitalTaipeiRepublic of China

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