Congenitally Corrected Transposition

Abstract

Congenitally corrected transposition of the great arteries is characterized by discordant atrioventricular and ventriculoarterial connections, with either normally positioned or mirror-image atria. Hence, the systemic venous return is conveyed through the morphological left ventricle into the pulmonary trunk, while the pulmonary venous return is directed through the morphological right ventricle into the aorta. The problems in patients with congenitally corrected transposition arise from the high incidence of associated anomalies. The most important such anomalies are ventricular septal defects, left atrioventricular valve (tricuspid valve) abnormalities, and pulmonary stenosis. An extensive review of congenitally corrected transposition was recently provided by Losekoot and associates [18].