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Comprehensive Diagnostic Criteria for IgG4-Related Disease

  • Hisanori Umehara
  • Kazuichi Okazaki
Chapter

Abstract

Although IgG4-related disease (IgG4-RD) is a novel and important disease entity characterized by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4-positive plasma cells, its clinical diagnostic criteria have not been fully established. Many patients with IgG4-RD have lesions in multiple organs, either synchronously or metachronously, and the pathological features of each organ differ. We established comprehensive diagnostic criteria for IgG4-RD for the practical use of specialists and nonspecialists.

Keywords

Autoimmune Pancreatitis Retroperitoneal Fibrosis Serum IgG4 Concentration Elevated Serum IgG4 Idiopathic Retroperitoneal Fibrosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Japan 2014

Authors and Affiliations

  1. 1.Department of Hematology and ImmunologyKanazawa Medical UniversityUchinadaJapan
  2. 2.Division of Gastroenterology and Hepatology, The third Department of Internal MedicineKansai Medical UniversityMoriguchi CityJapan

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