Abstract
Vanishing leukoencephalopathy is a vacuolating leukoencephalopathy with subcortical cysts. Symptoms develop at 18 months to 5 years of age with slowly progressive cerebellar ataxia, spasticity, variable optic atrophy, late development of bulbar symptoms, and preserved mental capacities. There are adult cases.
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18 Leukodystrophy
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(2007). Leukodystrophy. In: Pediatric Neuropathology. Springer, Tokyo. https://doi.org/10.1007/978-4-431-49898-8_18
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DOI: https://doi.org/10.1007/978-4-431-49898-8_18
Publisher Name: Springer, Tokyo
Print ISBN: 978-4-431-70246-7
Online ISBN: 978-4-431-49898-8
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