Chapter 3.26 Double discordance
In this fascinating cardiac malformation, the morphologically left atrium (=pulmonary venous atrium) is connected via a tricuspid valve with the morphologically right ventricle, from which originates the aorta, while the morphologically right atrium (= systemic venous atrium) is connected via a mitral valve with the morphologically left ventricle, from which originates the pulmonary artery. Therefore two discordant connections, atrioventricular and ventriculoarterial (= double discordance), occur in sequence in each side of the heart. The classical definition of “congenitally corrected transposition of the great arteries” derived from the observation that the effects of transposition of the great arteries are “corrected” by the congenital inversion of the two ventricles, with the two circulatory pathways “physiologically” in series, despite the anatomic derangements.
KeywordsTricuspid Valve Ventricular Septal Defect Great Artery Atrioventricular Valve Pulmonary Artery Banding
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