Double outlet right ventricle


Double outlet right ventricle defines a heterogeneous group of cardiac malformations unified by an abnormal ventriculoarterial connection. General agreement about the definition of double outlet right ventricle is when both great arteries, or one great artery and more than half of the other originates from the right ventricle. However, as clearly demonstrated with noninvasive investigations, this definition could be misleading due to the fact that the ventriculoarterial connections, lying on different planes, could be visualized in different ways, leading to different results, depending upon the orientation plan of the examination, independent of whether echocardiography, CT scan or MRI is used (Fig. 3.25.2). According to Yves Lecompte, the classification and terminology of this complex group of patients with anomalous ventriculoarterial connection is less important than the precise pre-operative definition of the anatomic criteria useful to determine the best surgical approach.


Aortic Arch Ventricular Septal Defect Pulmonary Valve Great Artery Arterial Switch Operation 
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  1. Bex JP, Lecompte Y, Baillot F, Hazan E (1980) Anatomical correction of transposition of the great arteries. Ann Thorac Surg 29:86PubMedCrossRefGoogle Scholar
  2. Borromée L, Lecompte Y, Batisse A, Lemoine G, Vouhé P, Sakata R, Leca F, Zannini L, Neveux JY (1988) Anatomic repair of anomalies of ventriculoarterial connection associated with ventricular septal defect. II. Clinical results in 50 patients with pulmonary outflow tract obstruction. J Thorac Cardiovasc Surg 95:96PubMedGoogle Scholar
  3. Choi BW, Park YH, Choi JY, Choi BI, Kim MJ, Ryu SJ, Lee JK, Sul JH, Lee SK, Cho BK, Choe KO (2001) Using electron beam CT to evaluate conotruncal anomalies in pediatric and adult patients. Am J Roentgenol 177:1045–1049Google Scholar
  4. Corno AF, Hurni M, Griffin H, Galal OM, Payot M, Sekarski N, Tozzi P, von Segesser LK (2002) Bovine jugular vein as right ventricle-to-pulmonary artery valved conduit. J Heart Valve Dis 11:242–247PubMedGoogle Scholar
  5. Corno AF, Bonnet D, Sekarski N, Sidi D, Vouhe PR, von Segesser LK (2003) Remote control of pulmonary blood flow: initial clinical experience. J Thorac Cardiovasc Surg 126:1775–1780Google Scholar
  6. Corno AF, Qanadli SD, Sekarski N, Artemisia S, Hurni M, Tozzi P, von Segesser LK (2004) Bovine valved xenograft in pulmonary position: medium-term follow-up with excellent hemodynamics and freedom from calcifications. Ann Thorac Surg 78:1382–1388PubMedCrossRefGoogle Scholar
  7. Dorfman AL, Geva T (2006) Magnetic resonance imaging evaluation of congenital heart disease: conotruncal anomalies. J Cardiovasc Magn Reson 8:645–659PubMedCrossRefGoogle Scholar
  8. Dos L, Pen V, Silversides C, Provost Y, Oechslin E, Horlick E, Paul N (2007) Images in cardiovascular medicine. Cardiac magnetic resonance imaging and multidetector computed tomography scan illustrating Damus-Kaye-Stansel operation. Circulation 115: e440–442PubMedCrossRefGoogle Scholar
  9. Goo HW, Park IS, Ko JK, Kim YH, Seo DM, Yun TJ, Park JJ, Yoon CH (2003) CT of congenital heart disease: normal anatomy and typical pathologic conditions. Radiographics 23:S147–165PubMedCrossRefGoogle Scholar
  10. Lecompte Y, Neveux JY, Leca F, Zannini L, Tu TV, Duboys Y, Jarreau MM, Starr A (1982) Reconstruction of the pulmonary outflow tract without prosthetic conduit. J Thorac Cardiovasc Surg 84:727–733PubMedGoogle Scholar
  11. Lecompte Y, Batisse A, di Carlo D (1993) Double-outlet right ventricle: a surgical synthesis. Adv Card Surg 4:109–136PubMedGoogle Scholar
  12. Sodian R, Weber S, Markert M, Rassoulian D, Kaczmarek I, Lueth TC, Reichart B, Daebritz S (2007) Stereolithographic models for surgical planning in congenital heart surgery. Ann Thorac Surg 83:1854–1857PubMedCrossRefGoogle Scholar
  13. Sorensen TS, Mosegaard J, Greil GF, Miller S, Seeger A, Hansen OK, Sieverding L (2007) Images in cardiovascular medicine. Virtual cardiotomy for preoperative planning. Circulation 115:e312PubMedCrossRefGoogle Scholar
  14. Uehara M, Funabashi N, Ogawa Y, Minamino T, Komuro I (2007) Double outlet right ventricle demonstrated by multislice computed tomography. Int J Cardiol 121:218–220PubMedCrossRefGoogle Scholar

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© Steinkopff Verlag 2009

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