Surgical Therapy for Moyamoya Disease

  • Jiro Suzuki


Moyamoya disease is a cerebrovascular disease in which vascular stenosis or occlusion of an unknown origin is seen in cerebral angiograms to extend from the termination of the bilateral internal carotid arteries (ICA) to the origin of the anterior and middle cerebral arteries (ACA and MCA). An abnormal, fine vascular network is also found at the base of the brain16, 43, 47, 49, 53, 54. Although there are cases in which basal moyamoya vessels are found in association with lesions of known etiology 25, 35, 36, 42, 60, such as von Recklinghausen’s disease 58, trauma 54, fibromuscular dysplasia (FMD)54, or atherosclerosis 34, when the etiology is known, it is not diagnosed as Moyamoya disease 54. Similarly, cases presenting only unilateral basal moyamoya vessels are not considered to be true Moyamoya disease, but are referred to as quasi-Moyamoya disease.


Cerebral Blood Flow Moyamoya Disease Superior Cervical Ganglion Superficial Temporal Artery Collateral Pathway 
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Copyright information

© Springer-Verlag/Wien 1987

Authors and Affiliations

  • Jiro Suzuki
    • 1
  1. 1.Division of Neurosurgery, Institute for Brain DiseasesTohoku University School of MedicineNagamachi, SendaiJapan

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