Haemangioblastoma, Haemangioblastomatosis, and von Hippel-Lindau Disease

  • F. Resche
  • J. P. Moisan
  • J. Mantoura
  • A. De Kersaint-Gilly
  • M. J. Andre
  • I. Perrin-Resche
  • D. Menegalli-Boggelli
  • Y. Lajat
  • S. Richard
Part of the Advances and Technical Standards in Neurosurgery book series (NEUROSURGERY, volume 20)


Haemangioblastoma is the archetypal vascular neoplasm of the central nervous system (CNS). Cytologically benign, it may occur either as a single lesions or as a multicentric tumour, as a sporadic case or as a familial disease. It constitutes the retinal and neuraxial component of von Hippel-Lindau (VHL) phakomatosis.


Stromal Cell Renal Clear Cell Carcinoma Posterior Cranial Fossa Intramedullary Spinal Cord Visceral Lesion 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.



Central nervous system


X-Ray computed tomography


Magnetic resonance imaging


red blood cells


von Hippel-Lindau


white blood cells


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Copyright information

© Springer-Verlag/Wien 1993

Authors and Affiliations

  • F. Resche
    • 1
  • J. P. Moisan
    • 2
  • J. Mantoura
    • 1
  • A. De Kersaint-Gilly
    • 3
  • M. J. Andre
    • 4
  • I. Perrin-Resche
    • 5
  • D. Menegalli-Boggelli
    • 1
  • Y. Lajat
    • 1
  • S. Richard
    • 6
  1. 1.Department of Neurosurgery, Centre Hospitalier Régional et Universitaire (CHRU)University of NantesFrance
  2. 2.Department of Molecular Biology, CHRU and Institut National de la Santé et de la Recherche Médicale (INSERM Unit 211)University of NantesFrance
  3. 3.Department of Neuroradiology, CHRUUniversity of NantesFrance
  4. 4.Department of Histology, Embryology, and Cytogenetics, CHRUUniversity of NantesFrance
  5. 5.Department of Nuclear Medicine, CHRUUniversity of NantesFrance
  6. 6.Department of Neurohistology, Ecole Pratique des Hautes EtudesHôpital de la SalpêtrièreParisFrance

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