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Haemangioblastoma, Haemangioblastomatosis, and von Hippel-Lindau Disease

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Book cover Advances and Technical Standards in Neurosurgery

Part of the book series: Advances and Technical Standards in Neurosurgery ((NEUROSURGERY,volume 20))

Abstract

Haemangioblastoma is the archetypal vascular neoplasm of the central nervous system (CNS). Cytologically benign, it may occur either as a single lesions or as a multicentric tumour, as a sporadic case or as a familial disease. It constitutes the retinal and neuraxial component of von Hippel-Lindau (VHL) phakomatosis.

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Abbreviations

CNS:

Central nervous system

CT:

X-Ray computed tomography

MRI:

Magnetic resonance imaging

RBC:

red blood cells

VHL:

von Hippel-Lindau

WBC:

white blood cells

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Authors and Affiliations

  1. Department of Neurosurgery, Centre Hospitalier Régional et Universitaire (CHRU), University of Nantes, France

    F. Resche, J. Mantoura, D. Menegalli-Boggelli & Y. Lajat

  2. Department of Molecular Biology, CHRU and Institut National de la Santé et de la Recherche Médicale (INSERM Unit 211), University of Nantes, France

    J. P. Moisan

  3. Department of Neuroradiology, CHRU, University of Nantes, France

    A. De Kersaint-Gilly

  4. Department of Histology, Embryology, and Cytogenetics, CHRU, University of Nantes, France

    M. J. Andre

  5. Department of Nuclear Medicine, CHRU, University of Nantes, France

    I. Perrin-Resche

  6. Department of Neurohistology, Ecole Pratique des Hautes Etudes, Hôpital de la Salpêtrière, Paris, France

    S. Richard

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Resche, F. et al. (1993). Haemangioblastoma, Haemangioblastomatosis, and von Hippel-Lindau Disease. In: Symon, L., et al. Advances and Technical Standards in Neurosurgery. Advances and Technical Standards in Neurosurgery, vol 20. Springer, Vienna. https://doi.org/10.1007/978-3-7091-6912-4_6

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