Xg System

  • Helmut Schenkel-Brunner


Discovered in 1962 [26], XG is the only known blood group system to be submitted by an X-borne gene. It comprises only one antigen specificity, Xg a, approximately 89% of all females and 66% of all males being Xg(a+) [28]. Two alleles of the XG gene have been postulated—the structural form X g a, which controls the formation of Xg a (= XG1) character (ISBT No. 012 001), and the silent form Xg, which is assumed to be responsible for the absence of Xg a in the Xg(a-) phenotype [28].


Primitive Neuroectodermal Tumor Pseudoautosomal Region Blood Group System MIC2 Gene Peripheral Primitive Neuroectodermal Tumor 
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Copyright information

© Springer-Verlag Wien 2000

Authors and Affiliations

  • Helmut Schenkel-Brunner
    • 1
  1. 1.Institut für Medizinische BiochemieUniversität WienViennaAustria

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