Neurofibroma, Neurofibromatosis

  • Mario Campanacci


Also a nerve sheath hamartona, the neurofibroma is constituted by Schwann cells and fibroblasts. Besides this histological difference (which is not always sharply defined), compared to neurilemoma the neurofibroma is not encapsulated, it is frequently multiple or plexiform, it frequently occurs in neurofibromatosis 1 and, in this case, it has a significant tendency to malignant transformation.


Schwann Cell Fibrous Dysplasia Malignant Peripheral Nerve Sheath Tumor Nerve Sheath Tumor Plexiform Neurofibroma 
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Copyright information

© Springer-Verlag Wien 1999

Authors and Affiliations

  • Mario Campanacci
    • 1
    • 2
  1. 1.University of BolognaItaly
  2. 2.Rizzoli Orthopaedic InstituteBolognaItaly

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