Abstract
Hypothalamic hamartoma (HH) is usually associated with refractory epilepsy, cognitive impairment, and behavioral disturbance. There is now increasing evidence that HH can be treated effectively with a variety of neurosurgical approaches. Treatment options for intractable gelastic seizure in HH patients include direct open surgery with craniotomy, endoscopic surgery, radiosurgery with gamma knife (GKS) and stereotactic radiofrequency thermocoagulation. Selection of treatment modalities depends on type and size of the HH and the surgeon’s preference. Two surgical techniques, resection and disconnection, had been described with favorable outcomes. Pretreatment evaluation, patient selection, surgical techniques, complications, and possible selection of treatment are discussed in this chapter.
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Acknowledgments
The authors thank Professor Tae-Gon Kim and Miss Sang-Hee Ahn for their help in preparing the manuscript.
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© 2012 Springer-Verlag Wien
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Choi, JU., Kim, DS. (2012). Treatment Modalities for Intractable Epilepsy in Hypothalamic Hamartoma. In: Akalan, N., Di Rocco, C. (eds) Pediatric Epilepsy Surgery. Advances and Technical Standards in Neurosurgery, vol 39. Springer, Vienna. https://doi.org/10.1007/978-3-7091-1360-8_5
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DOI: https://doi.org/10.1007/978-3-7091-1360-8_5
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