Abstract
Congenital diaphragmatic hernia (CDH) is a malformation characterized by a defect in the posterolateral diaphragm, the foramen of Bochdalek, through which the abdominal viscera migrate into the chest during fetal life. The reported incidence of CDH varies from 1 in 2200 to 1 in 5000 births. In most series, 80% of posterolateral diaphragmatic hernias have been reported to occur on the left side and 20% on the right side. Bilateral CDH is rare. The size of the defect varies from small (2 or 3 cm) to very large, involving most of the hemidiaphragm. A rim of muscle is usually present around the defect, which is often covered posteromedially with peritoneum. A hernial sac, composed of pleura and peritoneum, has been reported in about 20% of patients. Despite remarkable progress in resuscitation and intensive care, the mortality and morbidity in CDH still remains high. The high morbidity and mortality rates are attributed to severe lung hypoplasia and/or persistent pulomnary hypertension.
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Puri, P. (2019). Congenital Diaphragmatic Hernia and Eventration. In: Puri, P., Höllwarth, M. (eds) Pediatric Surgery. Springer Surgery Atlas Series. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-56282-6_14
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DOI: https://doi.org/10.1007/978-3-662-56282-6_14
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