Zusammenfassung
Der Terminus »vaskuläre Anomalien« umschreibt ein großes Spektrum von Erkrankungen vom einfachen »Geburtsmal« bis hin zu einer lebensbedrohlichen Erkrankung. Anhand einer einheitlichen Einteilung, der ISVVA-Klassifikation unterscheidet man die vaskulären Anomalien prinzipiell in vaskuläre Tumoren und vaskuläre Anomalien. Die Unterscheidung erfolgte in Anlehnung an das Erscheinungsbild sowie der radiologischen und pathologischen Merkmale. Vaskuläre Tumoren wachsen infolge einer zellulären Hyperplasie. Sie können je nach Typ wachsen, persistieren oder regressieren. Der häufigste Vertreter dieser Gruppe, das infantile Hämangiom, ist also ein benigner vaskulärer Tumor. Vaskuläre Malformationen hingegen sind das Ergebnis lokalisierter Defekte in der vaskulären Morphogenese, vermutlich infolge fehlerhafter Pfade im Rahmen der Embryo- und Vaskulogenese. Vaskuläre Malformationen regressieren niemals, sie bleiben zeitlebens bestehen. Sie wachsen während des Wachstums meist proportional mit.
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Neuhaus, K., Lenz, Y., Weibel, L., Rössler, J., Fattouh, M. (2017). Vaskuläre Anomalien. In: Schiestl, C., Stark, G., Lenz, Y., Neuhaus, K. (eds) Plastische Chirurgie bei Kindern und Jugendlichen. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-51391-0_26
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