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Pädiatrische Neurochirurgie pp 195–203Cite as

Chiari-Malformationen

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Zusammenfassung

Aktuell werden in der Literatur 5 verschiedene Chiari-Malformationen unterschieden (Grad 0–IV). Die einzelnen Chiari-Malformationen sind als komplett eigenständige Entitäten aufzufassen. Bei der Gruppe der Chiari-I-Malformationen können zusätzlich 5 Untergruppen unterschieden werden. Alle Chiari-Malformationen (außer Grad IV) bedingen eine Liquorpulsationsbehinderung aus der hinteren Schädelgrube in Richtung Spinalkanal. Ansonsten sind das klinische Erscheinungsbild, die bildgebenden Befunde und insbesondere die Therapie jeder einzelnen Form und Unterform verschieden.

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Authors and Affiliations

  1. Klinik für Neurochirurgie, Bundeswehrkrankenhaus Ulm, Ulm, 89081, Deutschland

    U. M. Mauer

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  1. U. M. Mauer
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Correspondence to U. M. Mauer .

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Editors and Affiliations

  1. Sektionsleiterin Pädiatrische Neurochirurgie, Neurochirurgische Klinik Universitätsklinikum, Heidelberg, Germany

    Heidi Bächli

  2. Universitätskinderklinik beider Basel (UKBB), Binningen, Switzerland

    Jürg Lütschg

  3. Chefärztin der Abteilung Kinderneurochirurgie Asklepios Kinderklinik, Sankt Augustin, Germany

    Martina Messing-Jünger

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Mauer, U.M. (2018). Chiari-Malformationen . In: Bächli, H., Lütschg, J., Messing-Jünger, M. (eds) Pädiatrische Neurochirurgie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-48700-6_17

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  • DOI: https://doi.org/10.1007/978-3-662-48700-6_17

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-48699-3

  • Online ISBN: 978-3-662-48700-6

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