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Prevention of Disorders of Hearing Development

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Phoniatrics I

Abstract

Universal newborn hearing screening (UNHS) has turned out to be the most effective way to identify congenital paediatric sensorineural hearing loss. Screening principles and methods, possible screening failures, management of control intervals, screenings for late-onset hearing loss and how to communicate the results of UNHS are core areas of the first section.

A brief overview is provided of some concepts and existing formal programmes that aim to support parents in enhancing parent-child communication skills.

Audiograms of family members can provide an indication of the type of hearing disorder and possible genetic causes. Affected relatives may profit from earlier diagnosis and intervention.

Genetic counselling is crucial in the diagnostic approach of hereditary hearing loss. Results of DNA testing should be explained to the patient, his parents and eventually other relatives by a clinical geneticist.

In conclusion, this chapter presents information on advice concerning hearing conservation, especially in the case of large endolymphatic duct and sac, and how to prevent noise- or music-induced hearing loss. The necessity to avoid noise in combination with ototoxic drugs is a further issue. Some general aspects are added.

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am Zehnhoff-Dinnesen, A. et al. (2020). Prevention of Disorders of Hearing Development . In: am Zehnhoff-Dinnesen, A., Wiskirska-Woznica, B., Neumann, K., Nawka, T. (eds) Phoniatrics I. European Manual of Medicine. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-46780-0_17

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