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Blistering Diseases pp 251–263Cite as

Epidemiology of Autoimmune Bullous Diseases

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Abstract

Autoimmune bullous diseases are a heterogeneous group of diseases also in terms of epidemiological characteristics. Recent high-quality epidemiological studies have provided valuable new knowledge in this area. It has become clear that the incidence of bullous pemphigoid in Central Europe has at least doubled over the last decade and that incidences of the different autoimmune diseases vary considerably between geographical regions. The increased mortality risk as well as the association with neurological diseases in patients with bullous pemphigoid has been highlighted in several studies, raising the intriguing question about the link between the neurological and skin diseases in affected patients.

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Acknowledgment

This work was supported by the Excellence Cluster “Inflammation at Interfaces” (EXC306/1; to E.S.), the European Community’s FP7 (Coordination Theme 1-HEALTH-F2–2008–200515), and the Swiss National Foundation for Scientific Research (31003A-121966 and 31003A-09811; both to L.B.).

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Authors and Affiliations

  1. Department of Dermatology, University of Lübeck, Luebeck, Germany

    Enno Schmidt MD, PhD

  2. Department of Dermatology, University Hospital, Inselspital, Bern, Switzerland

    Luca Borradori MD

  3. Department of Dermatology, CHU Charles Nicolle, Rouen Cedex, France

    Pascal Joly MD, PhD

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  1. Enno Schmidt MD, PhD
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  2. Luca Borradori MD
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  3. Pascal Joly MD, PhD
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Correspondence to Enno Schmidt MD, PhD .

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Editors and Affiliations

  1. Department of Dermatology, St George Hospital, University of New South Wales, Sydney, New South Wales, Australia

    Dédée F. Murrell

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Schmidt, E., Borradori, L., Joly, P. (2015). Epidemiology of Autoimmune Bullous Diseases. In: Murrell, D. (eds) Blistering Diseases. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-45698-9_21

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